產(chǎn)品名稱 PCCA Antibody from INVITROGEN ANTIBODIES
    產(chǎn)品貨號(hào) A304-324A-T
    產(chǎn)品價(jià)格 現(xiàn)貨詢價(jià)，電話：010-67529703
    產(chǎn)品規(guī)格 20 μL
    產(chǎn)品品牌 INVITROGEN ANTIBODIES
    產(chǎn)品概述
    產(chǎn)品詳情
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    Antigenic SpecificityPCCA
    Clonepolyclonal
    Host SpeciesRabbit
    Reactive Specieshuman, mouse
    Isotypen/a
    Formatpurified
    Size20 μL
    Concentrationn/a
    ApplicationsWestern Blot: 1:1,000
    Reviews / RatingsIf you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY.
    DescriptionPCCA Polyclonal Antibody. This protein is a key enzyme in the catabolic pathway of odd-chain fatty acids, isoleucine, threonine, methionine, and valine. It is probably a dodecamer composed of six biotin-containing alpha subunits and six beta subunits. The protein is located in the mitochondrial matrix. Defects in PCCA are the cause o fpropionic acidemia type I (PA-1) [MIM:606054]. PA-1 is a life-threatening disease characterized by episodic vomiting, lethargy and ketosis, neutropenia, periodic thrombocytopenia, hypogammaglobulinemia, develop-mental retardation, and intolerance to protein.
    Immunogenn/a
    Other NamesRP11-151A6.1
    Gene, Accession #Entrez: 110821, 5095; Uniprot: P05165, Q91ZA3
    Catalog #A304-324A-T
    Price
    Order / More InfoPCCA Antibody from INVITROGEN ANTIBODIES
    Product Specific Referencesn/a
    產(chǎn)品資料 
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