產(chǎn)品名稱 PCCA Antibody from INVITROGEN ANTIBODIES
    產(chǎn)品貨號(hào) PA5-71678
    產(chǎn)品價(jià)格 現(xiàn)貨詢價(jià)，電話：010-67529703
    產(chǎn)品規(guī)格 400 μl
    產(chǎn)品品牌 INVITROGEN ANTIBODIES
    產(chǎn)品概述
    產(chǎn)品詳情
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    Antigenic SpecificityPCCA
    Clonepolyclonal
    Host SpeciesRabbit
    Reactive Specieshuman, rat
    Isotypen/a
    Formatpurified
    Size400 μl
    Concentrationn/a
    ApplicationsImmunohistochemistry (Paraffin): 1:1000, Western Blot: 1:1000
    Reviews / RatingsIf you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY.
    DescriptionPCCA Polyclonal Antibody. This protein is a key enzyme in the catabolic pathway of odd-chain fatty acids, isoleucine, threonine, methionine, and valine. It is probably a dodecamer composed of six biotin-containing alpha subunits and six beta subunits. The protein is located in the mitochondrial matrix. Defects in PCCA are the cause o fpropionic acidemia type I (PA-1) [MIM:606054]. PA-1 is a life-threatening disease characterized by episodic vomiting, lethargy and ketosis, neutropenia, periodic thrombocytopenia, hypogammaglobulinemia, develop-mental retardation, and intolerance to protein.
    Immunogenn/a
    Other NamesPCCase alpha subunit; pccA complementation group; propanoyl-CoA:carbon dioxide ligase alpha subunit; propionyl Coenzyme A carboxylase; alpha polypeptide; propionyl-CoA carboxylase alpha chain; mitochondrial
    Gene, Accession #Entrez: 5095, 687008; Uniprot: P05165, P14882
    Catalog #PA5-71678
    Price
    Order / More InfoPCCA Antibody from INVITROGEN ANTIBODIES
    Product Specific Referencesn/a
    產(chǎn)品資料 
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